Sucessful dietetic-therapy in primary intestinal lymphangiectasia and recurrent chylosa ascites: a case report

Sucessful dietetic-therapy in primary intestinal lymphangiectasia and recurrent chylosa ascites: a case report
Nutr Hosp. 2007 Nov-Dec

Martín CC, García AF, Restrepo JM, Pérez AS.
Unidad de Nutrición Clínica y Dietética, Servicio de Endocrinología y Nutrición, Hospital Universitario Virgen Macarena, Sevilla, España. smaradigna@hotmail.com

OBJECTIVES: Primary intestinal lymphangiectasia is a lymphatic system's disorder, where lymphatic drainage is blockaged. Clinically it produces malabsorption, protein-losing enteropathy, hypogammaglobulin in blood, and several degrees of malnutrition. Its treatment is not easy and includes dietetic-therapy and drugs.

MATERIAL AND METHOD: A 35-year-old-woman case report is exposed. She has recurrent chylosa ascites, requiring several admissions and evacuatory paracentesis. After food-fat was replaced by medium-chain triacyl-glicerol-enriched diet, a clinical, analytical and anthropometric improvement was demonstrated.

CONCLUSSIONS: The major way of treatment in intestinal lymphangiectasia in this case is the employement of specific-diet and adaptaded-basic-food. It's difficult and high collaboration of the patient is required, being necessary medical revisions during the whole life, due to the not well known evolution of this long-standing disease.

PMID: 18051999 [PubMed - in process]

Remission of protein-losing enteropathy after nodal lymphoma treatment in a patient with primary intestinal lymphangiectasia.

Remission of protein-losing enteropathy after nodal lymphoma treatment in a patient with primary intestinal lymphangiectasia.
Eur J Gastroenterol Hepatol. 2005 Dec

Laharie D,
Degenne V,
Laharie H,
Cazorla S,
Belleannee G,
Couzigou P,
Amouretti M.
Service d'Hepatogastroenterologie, Hopital Haut-Leveque, Pessac, France. david.laharie@chu-bordeaux.fr

Primary intestinal lymphangiectasia (PIL), so-called Waldmann's disease, is an uncommon condition, characterized by dilated intestinal submucosal and subserosal lymphatics of the gastrointestinal tract. Protein-losing enteropathy is the most common manifestation of this supposed congenital disease. Since the initial description in 1961, 11 cases of lymphoma have been reported suggesting that PIL predisposes to lymphoma. Here, we report the first case of primary nodal location lymphoma during PIL with recovery of the protein-losing enteropathy after its treatment by radiochemotherapy.

Lippincott Williams & Wilkins