Intestinal lymphangiectasia associated with recurrence of histiocytosis X.

Sept 2011

Hui CK.

Source

Centre for Alimentary Studies, 5/F Century Square, 1 D'Aguilar Street, Central, Hong Kong SAR, China. bckhui@gmail.com

Abstract

K e y w o r d s : h i s t i o c y t o s i s X , i n t e s t i n a l

lymphangiectasia, secondary cause

Intestinal lymphangiectasia may occur as a primary congenital disorder or a secondary disorder. Secondarylymphangiectasia could be associated with diseases such as abdominal carcinoma, retroperitoneal fibrosis or chronic pancreatitis. This is the first reported case of intestinal lymphangiectasia associated with recurrent histiocytosis X. This case report illustrates the need for more prospective, well-designed studies to determine the natural history and outcome of intestinal lymphangiectasia in the duodenum. Hopefully, these studies will also help clinicians identify which group of patients with intestinal lymphangiectasia in the duodenum is more likely to have a secondary cause.

SMJ